Isolated Non-Compaction of Right Ventricular Myocardium, A Rare Congenital Anomaly and Role of Echocardiogram: A Case Report
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Abstract
The ventricular non-compaction or spongy myocardium is a rare congenital cardiomyopathy which is caused by defective morphogenesis of myocardium during embryonic life. It is characterised by excessive, coarse trabeculations within ventricular myocardium beyond papillary muscle insertion which communicates freely with the ventricular cavity. This carries high risk for development of serious arrhythmia, thromboembolic stroke, pump failure etc. Isolated LV involvement is the most common presentation (68%) and biventricular involvement is the next most common presentation (22-38%). Isolated non-compaction of RV myocardium is a rare anomaly. We are hereby presenting such a case.
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Stollberger C, Finsterer J, Blazek G (2002) Left ventricular hypertrabeculation/noncompaction and association with additional cardiac abnormalities and neuromuscular disorders. Am J Cardiol 90: 899-902. Link: https://bit.ly/2WpvG6m
Chin TK, Perloff JK, Williams RG, Jue K, Mohrmann R (1990) Isolated noncompaction of left ventricular myocardium. A study of eight cases. Circulation 82: 507-513. Link: https://bit.ly/2LndyDM
Junga G, Kneifel S, Von Smekal A, Steinert H, Bauersfeld U (1999) Myocardial ischaemia in children with isolated ventricular non-compaction. Eur Heart J 20: 910-916. Link: https://bit.ly/35SJB8a
Ulusoy RE, Karslan N, Kirilmaz A (2006) Non-compaction of ventricular myocardium involving both ventricles. Eur J Echocardiography 7: 457-460. Link: https://bit.ly/2WRtZxu
Cavusoglu Y, Ata N, Timuralp B, Gorenek B, Goktekin O, et al. (2003) Noncompaction of the ventricular myocardium: report of two cases with bicuspid aortic valve demonstrating poor prognosis and with prominent right ventricular involvement. Echocardiography 20: 379-383. Link: https://bit.ly/2LhEEfL
Oeschslin E, Attenhofer C, Rohas J, Kauffman P, Jenni R, et al. (2000) Long term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am CollCardiol 36: 493-500. Link: https://bit.ly/2YWIvqu
Jenni R, Oechslin E, Schneider J, AttenhoferJost C, Kaufmann PA (2001) Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction: a step towards classification as a distinct cardiomyopathy. Heart 86: 666-671. Link: https://bit.ly/2YUfT15